Hemosiderosis nke akpa ume: Mgbaàmà na ọgwụgwọ

Hemosiderosis nke akpa ume - a nnọọ oké ọrịa. Ọ na-adị mgbe a uka nke mkpụrụ ndụ ọbara uhie na kọntaktị na anụ ahụ nke ụmụ mmadụ na akpa ume. Mgbe a na-aga n'ihu n'ihi na a ogologo oge na mmepe nke hemosiderin ink nwere ígwè.

Gịnị bụ hemosiderosis?

Nchọpụta a na ọrịa bụ na o kwere omume na na ndabere nke X-ray, Otú ọ dị, e nwere ọtụtụ ihe mgbaàmà maka nke ya edidu nwere ike chere. Pụrụ iche ihe ịrịba ama na onye ọrịa gemosiderkoz akpa ume - a ọjọọ ụkwara, hawking ruo ọbara, mkpụmkpụ nke ume, na-agba ọbara na ngụgụ. E nwere ike ịbụ a fever na tachycardia.

Na ndabere nke X-ray nke akpa ume dọkịta nwere ike ime ka a anya nchoputa. ọzọ ọmụmụ na-mụụrụ iji gosi na onye ọrịa na-ata ahụhụ site na a na ọrịa bụ. Ọ bụ nnyocha nke sputum, ọbara onwu, n'oké ikpe - akpa ume biopsy.

Ọgwụgwọ nke ọrịa na-emepụta site na ngwa nke corticosteroids na ọgwụ ọjọọ na-ewepụ kpọmkwem ihe mgbaàmà.

ngosipụta nke ọrịa

Mgbawa akpa ume hemosiderosis a na-akpọ syndrome uduak-Gellerstedta. Nke a bụ a-enweghị nchịkwa na nsogbu, nke na-egosipụta onwe ya dị ka a N'ihi nke a pụrụ iche ink hemosiderin deposition na mmadụ akpa ume. The isi mma nke a ink na eziokwu na ọ mejupụtara ígwè oxide. Ọ bụ maka na nchekwa nke ígwè ke idem. N'oge ọrịa dị iche iche na ọ accumulates na anụ ahụ, nke na-eduga ná ọrịa nsogbu ahụ. Ọzọkwa, ọ pụrụ ịnọ na-ahụ mmadụ.

Na ya isi, hemosiderin - forms echekwara na ahụ mapụtara ígwè. N'ihi nke a na-akpa ákwà nwere a akpọ nyụrụ hue. Mgbe mmadụ na-amalite mgbawa akpa ume hemosiderosis, na anụ ahụ nke ahụ pụrụ ịnọ na-ise grams ígwè.

Site n'onwe ya ígwè ìgwè adịchaghị emetụta ịrụ ọrụ nke bụ isi ndị na nke ahụ, na nke a na-akpa ume. Otú ọ dị, ọ bụrụ na esonyere akpa ume hemosiderosis sclerosis, ọtọ ọrịa na ahụ apụghị izere ezere.

Na n'ihe ize ndụ ọrịa susceptible ka ọrịa a na-eto eto ụmụ na-eto eto. Ọtụtụ mgbe nwanyị.

Na-akpata ọrịa

Hemosiderosis nke akpa ume nwere ike ime na ụmụ mmadụ dị iche iche ihe. The kasị - a congenital nkwarụ na arịa mgbidi nke akpa ume mgbasa. N'ihi nke a, na ahụ e a depletion nke capillaries na-adịru nwa oge cessation nke ọbara. N'ihi ya exuded erythrocytes, na akpa ume na nsụkọrọ Ugboro akpa ume microbleeds.

Dị ka a N'ihi nke a bụ na ígwè na tọhapụrụ na adaghị hemosiderin. Ọ, n'aka nke ya, na-etinye obi gị dum site alveolar macrophages na edebe ke epithelia na endothelial mkpụrụ ndụ na a nnukwu ngafe. Ọzọkwa na-egwuri a fateful ọrụ ọzọ congenital nkwarụ. Ezughị oke njikọ n'etiti anụ ahụ abụọ, na nke a - na bronchial akwara ndị gara na veins nke akpa ume.

Immunoallergic ọdịdị nke ọrịa

Akpata na morphogenesis nke akpa ume hemosiderosis nwekwara ike ịbụ immunoallergic. Mgbe a dịghịzi okụre ime ka emebi isi mgbidi nke akpa ume capillaries. E nwere a mebiri nke ha nkịtị ọrụ, site na mebiri emebi ọbara arịa na akpa ume na-ada ngafe ígwè, n'ihi aru ọrụ kpọrọ nsogbu n'obi.

Ọzọkwa, oké deposition nke hemosiderin na akpa ume anụ ahụ na-eme ka otutu oge usoro mbibi nke mkpụrụ ndụ ọbara uhie, Bilie ntọhapụ nke haemoglobin, nke pụtara na splin. A elu nke ígwè absorption ke gootu, ruo ogologo oge iji ọgwụ na a elu ígwè ọdịnaya.

Mgbe mbụ ogbo nke akpa ume hemosiderosis na ụmụ nwere ike ime ka ihe mgbawa ọrịa na-adịghị metụtara nsogbu ndị ọzọ. A nwere ike so na syndrome Gainer (na ikpe ma ọ bụrụ na ahụ bụ kwa chebaara edozi ẹdude ke eke Bovine mmiri ara ehi).

Ọ bụrụ na hemosiderosis emee ọzọ, akpa ume mikrokrovotecheniya pụrụ iduga ọbara mgbali elu, nke nwere ike ibu a-adịghị ala ala nsogbu.

Ọzọkwa, ọrịa nwere ike so na syndrome nke Goodpasture. Nke a mmeri nke alveoli nke ngụgụ na-na akụrụ, Bilie ha n'ichihịa. The ọrịa bụ na-emekarị n'okpuru ndị ikom dị afọ 20 ruo afọ 30. E nwere otu echiche banyere ya butere n'aka okike.

agaghinihu hemosiderosis

Mgbawa akpa ume hemosiderosis na ụmụaka a na-triggered site na-efe efe. O nwere ike ịbụ dị ka mfe SARS, nakwa dị ka ihe dị oké njọ ọrịa - Measles, whooping ụkwara na ịba. Ọzọkwa, ọ pụrụ ịbụ ndị na-esi nke igbu egbu.

Agaghinihu hemosiderosis amalite na-adịghị ala ala obi nsogbu. O nwere ike ịbụ ụdị nile nke gbasara obi ọrịa - obi ọrịa, cardio na ọrịa ndị ọzọ.

Ugboro akpata ugboro ugboro na agaghinihu hemosiderosis protrude ogologo ikpughe na ala okpomọkụ, ike anụ ahụ ma ọ bụ iche echiche nje, ojiji nke ụfọdụ ọgwụ.

Ọ bụrụ na hemosiderosis aga n'ime alveoli nke akpa ume, na foto doro anya na anya metụtara nke microbleeds na ebe oké ego nke hemosiderin ndị yiri nodules, nke na-ndokwa si center na mpụta nke akpa ume.

mgbaàmà

Hemosiderosis nwere ike ime dị iche iche. Nnukwu, subacute na ntighari. Ọ bụrụ na ọrịa na-hụrụ na ụmụ, ọtụtụ mgbe ọ na-adị dị ka n'oge dị ụlọ akwụkwọ ọta akara afọ, ebe ọ bụ na afọ atọ. Otú ọ dị, e nwere ọrịa na onye nchoputa na-etinye na akpa izu nke ndụ.

Egosiwokwa ọrịa akpa ume hemorrhage na agba ọbara, mmetụta nke akụkụ okuku ume na ọdịda.

N'oge omume nke nsogbu na ụmụ mmadụ na-egosi arọ ụkwara nyụrụ agba, na oké ikpe, nwere ike coughing elu ọbara. Na-eto eto ụmụ, na ọbara nwere ike ịbụ na igbo.

On ule, ndị dọkịta ntị wheezing, tachycardia, fever, mgbe mgbe, ọrịa ọdọhọde nke ihe mgbu na obi na afo, nakwa na nkwonkwo. Ọ nwekwara ike ịbụ ndiiche ịmụba ọnụ ọgụgụ nke na imeju na-a nkọ dobe na ibu ibu.

Ọ bụrụ na hemoptysis na-aga n'ihu n'ihi na a ogologo oge, na-enwe ndidi na-amalite anaemia, n'adịghị ike na dizziness. The akpụkpọ aghọ chanwụrụ, na gburugburu anya na e nwere ihe e ji mara yellowness. The nwoke na ike gwụrụ ngwa ngwa na nọgidere na-anụ a mkpọtụ na nti. Arọ oge nke ọrịa nwere ike ime site na a awa ole na ole 10-15 ụbọchị. Ya mere, e nwere ike ime na-enweghị ọgwụ.

Mgbe oge nke na-akawanye njọ ụkwara na iku ume ọkụ ọkụ nwere ike ibelata, ma ọ bụ ike na-agba ya ume, ka ha hụ dọkịta a chọrọ ozugbo. Na mkpesa ngbaghara nwere ike ọgaghị adị na niile, onye bụ onye pụrụ iduga a full ndụ irè.

Na onye ọ bụla exacerbation nke ọrịa ngbaghara oge na-ebelata, ma hà na-amụba oge na ogo nke ọdụdọ. Otu nke na-esi nke anaemia - ngụkọta depletion nke ahu. Na obere okwu, ọbụna ekwe omume ọnwụ nke onye ọrịa - a mwute nwere ike ime eme n'ihi na nke nnukwu akpa ume hemorrhage na mberede akụkụ okuku ume na ọdịda.

nchoputa hemosiderosis

Iji n'ụzọ ziri ezi ịchọpụta akpa ume hemosiderosis, ị chọrọ onye ọkachamara uche nke ọtụtụ ndị ọkachamara. Mbụ niile, ọ bụ pulmonologist, hematologist. Na-mkpa na-amụ na-adakarị ngosipụta nke ọrịa. Nwere ike ime na-enweghị ihe ọmụmụ banyere X-ụzarị, sputum analysis, ọbara (dị ka a n'ozuzu analysis, na Biochemical) na akpa ume biopsy.

Nchọpụta ọrịa a bụ oké ike. Ọtụtụ mgbe iwe ọtụtụ ọnwa ma ọ bụ ọbụna ọtụtụ afọ tupu ọkachamara ịmata kpọmkwem a nchoputa. Mgbe ụfọdụ na-etinye ya mgbe ọ nwụsịrị. Ihe bụ na mbụ abụghị kpọmkwem ihe mgbaàmà, yiri ọtụtụ ọrịa ndị ọzọ, na ọtụtụ dị adịghị enye ha uru. Na-emekarị na ọ bụ nanị a akụkụ okuku ume na ọrịa so site ụkwara na anaemia.

nnukwu adọ

Ọ bụrụ na dọkịta chọpụtara mgbawa akpa ume hemosiderosis, ọgwụgwọ dị mkpa. The ahụ n'onwe ya apụghị ịnagide nsogbu a. Na nnukwu ụdị ọrịa na-esonyere crackles na palpitations. N'otu oge ahụ belatara larịị nke mkpụrụ ndụ ọbara uhie, elu bilirubin etoju nke ọbara ígwè na na ọbara ya bụ ntakiri.

N'oge ọdụdọ ime leukocytosis, ESR larịị adahade, nke na-emekarị na-egosi na mbufụt. Na mgbe e mesịrị nkebi nke ọrịa na-egosi polycythemia. Ọ bụ a benign akpụ usoro, Bilie hyperplasia nke ụmị ọkpụkpụ mkpụrụ ndụ.

X-ray ọmụmụ

Ke ọmụmụ ndị X-ụzarị ná mmalite nkebi nke ọrịa ji a ọnụ nke nghọta nke akpa ume ubi. N'otu oge, na atọ na nke anọ nkebi rụrụ ufiop agbawanye ọchịchịrị na ọnya nke connective anụ ahụ na e ji mara scars.

Ọtụtụ mgbe e nwere ọhụrụ Baịbụl hiwere isi n'ebe onyinyo, n'agbanyeghị eziokwu ahụ ochie akwụsị. On spirography o akụkụ okuku ume na nsogbu, na ngwá - miokardiostrofiya. Final nchoputa enyere akpa ume biopsy.

hemosiderosis ọgwụgwọ

Ihe ịga nke ọma ọgwụgwọ nke ọrịa a bụ nanị kwe omume mgbe ogologo oge ọgwụgwọ ọmụmụ nke corticosteroids. Ka ihe atụ, "Prednisolone" na-enyere gwọọ akpa ume hemosiderosis. The ọgwụ na-ebenata na permeability nke ọbara arịa na-egbochi mmepe nke autoimmune Jeremaya mere.

Ọ bụrụ na mgbanwe agwọ ọrịa na-ghọtara na-adịghị ike, mgbe ahụ, ịwa ahụ ụzọ na-eji. Nwere ike n'ụzọ zuru ezu ma ọ bụ na-ezughị ezu wepụrụ splin, ọ nwere ike budata belata ihe ize ndụ nke remissions. Ọzọkwa ọ na-ebelata likelihood nke ọdụdọ, na ọrịa ndu ndimmadu mgbe a na ime ga-amụba site 7-10 afọ.

Preparations na nnukwu na-adọ nke ọrịa development

Ọ bụ ihe kwesịrị ịrịba ama na nnukwu na-adọ na mgbochi nke yiri ọgwụ ọjọọ ọgwụ. Mgbe nchoputa nke "akpa ume hemosiderosis" n'imeso omume n'ụzọ dị irè site na a Nchikota cytostatic elekọta mmadụ na plasmapheresis. Nke a na-ebelata ọdịdị ọhụrụ autoantibodies na enyere ahụ ịnagide ochie.

Ọ bụkwa ihe dị irè usoro - mwepụ nke ígwè na mmamịrị, na-eji maka nke a infusion "Desferal". Na ọgwụgwọ nke mgbaàmà na-eji bronchodilators, antikoagulyarnye pụtara.

Ogologo oge ngbaghara dọkịta nwere ike nweta, mgbe n'ihe banyere ọrịa ha ka ha a na nlezianya nri na Ewezuga niile ngwaahịa dabeere na mmiri ara ehi. Ọ bụrụ na ọrịa ahụ asọpụta n'ime ala ala ogbo, ikekwe nhọpụta nke nitrati. Ọ bụ karịsịa metụtara na-adịghị ala ala obi nsogbu.

ụdị hemosiderosis

Dọkịta nwere ọtụtụ iche nke ọrịa a. Karịsịa, akpa ume hemosiderosis ji (macropreparations "Brown induration ìhè"). Na nke a, ngụgụ ntọt ke size, nwere nnọọ oké udidi. Ọzọkwa, ọchịchịrị-acha ọbara ọbara na agba aja aja na nso na sectional kwesiri ngosi whitish oyi akwa na brownish inclusions.

O nwekwara ike ime hemosiderosis akpa ume (micropreparations № 111). Na nke a, aja aja pigments anya n'ime sel na n'èzí na n'oge laabu mmeghachi omume Perls ibu-acha anụnụ anụnụ ma ọ bụ greenish. Ha bilie n'etiti bronchi na alveoli cavities.

Ọzọkwa, ndị a arịa ndị mmadụ akpa ume bụ nnọọ ikpọ na congested. The ọrịa na-esonyere ukwuu ọbara ọgbụgba n'ime nkebi n'etiti alveoli. N'otu oge ahụ ha na-chọpụtara oyi akwa nke connective anụ ahụ.