Eisenmenger syndrome: mgbaàmà. Eisenmenger syndrome na ime. Ọrịa na Eisenmenger syndrome

Demonstrable ọganihu na nkà mmụta ọgwụ na n'oge gara aga afọ ole na ole na-mere ka a nkọ na-abawanye na ndu ndimmadu, ma ọ bụ mkpochapu gbasara obi pathologies. Ke adianade do, na uzo nke XIX-XX ọtụtụ narị afọ, ndị ọkà mmụta sayensị kwuru na ọtụtụ ọrịa ndị ọhụrụ. The ihe mere ụfọdụ n'ime ha ka na-anọgide na a omimi, mgbaàmà - bịara ikiri, na ọgwụgwọ bụ nnọọ ike. Eisenmenger syndrome, a na-akpọ site aha nke Austrian pediatrician na cardiologist, ike-atụle nkịtị. Na-adịghị ahụkebe daa ọrịa natara a nkọwa zuru ezu banyere 100 afọ gara aga. Otú ọ dị, ọbụna taa, na-enweghị ka na-ekwu banyere a nghọta doro anya nke ya etiology.

ozi izugbe

Ọrịa (akpọ mgbe ụfọdụ mgbagwoju) Eisenmenger - a dị nnọọ ize ndụ daa ọrịa, inyịme na akpa ume na gbasara obi usoro. Gbasara obi ọrịa e ji ngụkọta ventricular septal nkwarụ , na ọbara mgbali. ọrịa na mmepe-eduga ụba nsogbu na emeghasịkwa na akpa ume mgbasa. N'ihi bụ a shunt, nke bụ maka ọbara nri ikike ekpe, nke na-emegide iwu ahụ nkịtị Filiks hemodynamics.

Ọzọkwa, echiche nke Eisenmenger syndrome-agụnye ọ bụla ọrịa obi, ọrịa ji emeghe atrioventricular kanaal na patent ductus arteriosus, ọnụnọ nke naanị otu ventricle. N'etiti ọrịa na ndiiche ventricular septal daa ọrịa na-chọpụtara na 10% nke ikpe. Na Ọdịdị nke congenital ntụpọ isi ahụ uru Eisenmenger mgbagwoju bụ 3%.

Akpata nke syndrome development

Single-akpata mmepe nke ọrịa, ndị dọkịta nwere ike ọ gaghị na-akpọ. Otú ọ dị, e nwere ọtụtụ ihe ndị etiological ihe na-amụbakwa ohere nke nwere ụmụ na Eisenmenger syndrome:

1. Butere n'aka pụrụ ịrịa. Imebi na site n'usoro larịị nwere ike gafere site nne na nna na nwa, si otú na-eme ihe mụbara ohere nke na-emepe emepe ọrịa obi.
2. Environmental ihe:

• mmenaanya nke nwa ebu n'afọ na utero;
• ruo ogologo oge n'ebe akpa radieshon;
• -adịghị ala ala na-efe efe na ọrịa nke a nne na nna;
• mmetụta nke ọgwụ na dietary Mmeju-eji ndị inyom n'oge ime.

Ihe ndị a bụ bụghị ahụkarị nnọọ maka Eisenmenger syndrome, ma ozizi ha nwere ike ịbụ ihe na-akpata dị iche iche pathologies, gụnyere nke a.

Dị ka ọrịa na-amalite?

Ọrịa na Eisenmenger syndrome-emekarị adịghị mkpesa nke nsogbu ahụ ike. Ya mere, n'oge nchoputa bụ bụghị mgbe niile kwere omume. The nwa mbụ attaches compensatory usoro, ma mgbe oge ụfọdụ ọrịa na-egosipụta onwe. Esịtidem ego ada ada, na-gbasara obi usoro gwụsịrị. Gịnị bụ Eisenmenger syndrome mgbaàmà?

1. Mụbara adịghị ike, njọ mgbe ihe omumu.
2. Mgbu na n'aka ekpe nke obi.
3. Ịba n'ehihie blueness nke anụ.
4. Spontaneous syncope.
5. Mmegide nke ụkwara na ọbara n'ahụ.

Ndị dị otú ahụ ihe mgbaàmà na-echegbu ọlị niile. The syndrome ruo ogologo oge pụrụ ịzụlite ngwa ngwa. Ọ bụrụ na a pediatrician onye na-elekọta nwa ahụ, na-atụ aro na-agafe ihe ọzọ nnyocha na Cardiology center, ha na-ekwesịghị ileghara.

Prenatal elekọta n'oge ọrịa

Russian dọkịta kweere na Eisenmenger syndrome na ime chere. Ya mere, n'oge ọ bụla na ogbo nke a nwaanyị na-ete ime na-atụ aro. Ha Western ọrụ ibe-eche ma ọ bụghị. Dị ka ha, na-agaziri ọgbọ adabere na nnabata ya na a set nke iwu na-atụ aro.

The nwaanyị mbụ ụlọ ọgwụ maka dum oge nke afọ ime. N'ụlọ ọgwụ ahụ, ndị dọkịta mkpa mgbe niile nyochaa ọnọdụ nke nwa ebu n'afọ na tụọ mgbali na akpa ume capillaries. Ke akpa ihe ịrịba ama nke iku ume ọkụ ọkụ - oxygen masks. Malite site na abụọ trimester kenyere ọgwụgwọ coagulants. A ụbọchị ole na ole tupu atụ anya ụbọchị nke omume nke nwa na-atụ aro ujo ọgwụ nke digitalis ịnọgide na-enwe gbasara obi usoro. Nnyefe bụ omume naanị na a eke ụzọ.

Ọ bụrụ na a nwaanyị kwesịrị-na niile chọrọ nke dọkịta, gbasara nke puru omume a mma pụta n'ihi na nwa bụ 50-90%. The amụma bụghị dị ka eme ka nne ya. Ọ bụ ya mere, mgbe ị na-ekpebi na n'ihu nke afọ ime, a nwaanyị kwesịrị-eche banyere nwere ihe ize ndụ.

Medical ule

Irè ọgwụ maka ọrịa na Eisenmenger syndrome bụ omume ka ewere enweghị a pụrụ iche ule. Ọ nwere ike na-aga na pụrụ iche clinics na kwesịrị ekwesị akụrụngwa. Ọ bụrụ na ị na-enyo na nke a daa ọrịa echetakwa omume na-emekarị na-agụnye:

• obi radiograph (atụmatụ mgbanwe akpa ume akwara na contours nke obi);
• angiography (vaskụla ọmụmụ);
• ECG (mata zoro ezo obi n'afọ iri na ụma na-enwe nsogbu);
• Echocardiography (anya nke enweghị nchịkwa mgbanwe mgbidi nke ventricles);
• gbasara obi catheterization (ntule nke ọrịa na odidi nke unan, mmesho nke space parameters nke isi akwara).

Esi nchoputa bụ amanyere bụ iwu niile ọrịa na-enyo enyo na Eisenmenger syndrome. Pentad Fallot, akwara stenosis, patent ductus arteriosus - a obere ndepụta pathologies ewepu.

ọgwụ ụkpụrụ

Conservative ọgwụgwọ nke ọrịa bụ na o kwere omume, ma ọ bụghị rụọ ọrụ nke ọma. N'aka nke ọzọ, na ojiji nke ịwa ahụ aka ọ bụghị mgbe nile ịrụpụta ezi ihe. Ya mere, taa, ndị dọkịta na-esiwanye iji Nchikota atụmatụ.

Ọrịa na a akpọ adakarị picture na ụba hematocrit họpụtara phlebotomy. The usoro a ugboro ugboro ruo ugboro atọ n'afọ, n'otu oge ya dị oké mkpa iji nyochaa ọbara ígwè kwa. Oxygen ọgwụ na anticoagulant ọgwụgwọ na-adịkarịghị eji, kama ịnara. Isi drawback nke ndị a na usoro a na-ewere a ọnụ ọgụgụ buru ibu nke mmetụta, kasị dị ịrịba ama n'etiti ndị nke bụ a hemorrhagic diathesis. Ọzọkwa, ọrịa ọgwụ na ọgwụ ọjọọ. "Epoprostenol" na "Treprostinil" mma hemodynamics na "Traklir" ebelata vaskụla eguzogide.

Surgery a rụrụ na abụọ variants: na nkunye nke a pacemaker, plastic nkwarụ MPP. Mgbe Eisenmenger syndrome ime ihe nwere ike budata melite prognosis nke ọrịa. Ọ bụrụ na ndị a si agwọ ọrịa na-adighi ike, nwere ike na-enyere ndị imekotaotuugbo transplantation nke ngụgụ na n'obi. Transplantation ịwa ahụ bụ Wezuga mgbagwoju anya, na-achọ nnukwu ego na-akwụ ụgwọ. N'aka nke ọzọ, ọ na-adịghị ewepụ ihe ize ndụ nke nsogbu. Mgbe ọ bụla ọzọ ngwọta, ihe ajụjụ bụ n'ụzọ kwụ ọtọ, abụọ transplant nwere ike ịzọpụta ndụ. Tupu ya, mmejuputa iwu dị mkpa na-agafe a mgbagwoju ọgwụ nnyocha.

Olee otú ọrịa na Eisenmenger syndrome?

Ndị na-obibi nke a gbasara obi ọrịa, mgbe mgbe-arụsi ọrụ ike ndụ. Otú ọ dị, ha nwere mgbe niile na-aga na nke dọkịta ma nyochaa ahụ ike egosi. Ndị dị otú ahụ ọrịa kwesịrị izere akpịrị ịkpọ nkụ, ruo ogologo oge n'ebe elu-efe efe. Ọ dị mkpa na-enye elu àgwà ọjọọ ma na-ewere ọgwụ na nwere ike ime ka ọbara na-agba. Ọ bụrụ na onye ọrịa ndị dọkịta iwu, ihe gbasara nke puru nke ekwe omume na-ebi ezigbo ndụ na-abawanye. Ma ọ bụghị ya, ọbara oxygen larịị nwere ike ịda na oké egwu-etoju na-eduga n'ọnwụ.